As well known, the original classic triad of features of Klippel-Feil syndrome are a short neck, a low posterior hairline, and a restricted range of motion of the neck, Certain of these patients are prone to associated abnormalities of the central nervous system as well as central stenosis and stenosis of the intervertebral foramen. It is reporting the risks for neurological damage are due to abnormalities other than the fusion pattern of the cervical vertebrae, commonly, However, the possibility of quadriplegia resulting from a minor injury of the neck in a patient with the Klippel-Feil syndrome accompanied with congenital malformation of vertebral artery in the proximal cervical spines. The purpose of this paper is to report a case of quadriplegia occurring in a patient with the Klippel-Feil syndrome having congenital vertebral artery malformation after only minor neck trauma, and to call attention to this particularly dangerous problem in such patients.

Keywords :Klippel-Feil syndrome, Vertebral artery malformation, Quadriplegia