Arthrogryposis Multiplex Congenita is a very rare disease which present at birth and non progress in character.

This disorder is characterized by limitation of motion of the joints of the extremities involved and appearance of marked wasting, due to diminished muscle substance, increased fibrous tissue about the joints, distrbance of joint mobility, and characteristic deformity.

This paper reports one case of arthrogryposis. The characteristic clinical aspects of joint deformities, laboratory and electromyographic findings are presented with a review of literature.

Keywords :Arthrogryposis multiplex congenita, Electromyography, Deformity