Neurilemmoma is benign neurogenic tumor which arise from the sheath of Schwann, its incidence on cervical nerve root are very rare. The patient with cervical root involvement presents pain or sensory disturbances of the upper extremity, neck, and/or chest wall. Usually, symptoms caused by pressure on the sensory and motor nerve roots with tumor mass. We report a patient with C8 dorsal nerve root neurilemmoma, with the brief review of literature.